Background: Rapunzel syndrome is an extremely rare intestinal condition in humans resulting from eating hair (trichophagia) . Rapunzel syndrome presents a rare type of trichobezoar with an extension of the hair into small bowel Case presentation: We present a three year old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all. The history of disease was similiar with celiac disease even though serology was negative. 

Conclusion: In children with a long history of gastrointestinal symptoms,upper digestive endoscopy is a cornerstone of Rapunzel syndrome as a diagnostic tool (in our case for another objective).Open surgery remain the mainstay of large thricobezoar removal Bezoar; Trichotilomania; Tricotillofagia; Trichobezoar; Rapunzel Syndrome

Rapunzel syndrome is an extremely rare intestinal condition in humans resulting from eating hair (trichophagia) . Rapunzel syndrome presents a rare type of trichobezoar with an extension of the hair into small bowel Case presentation: We present a three year old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all. The history of disease was similiar with celiac disease even though serology was negative. 

Conclusion: In children with a long history of gastrointestinal symptoms,upper digestive endoscopy is a cornerstone of Rapunzel syndrome as a diagnostic tool (in our case for another objective).Open surgery remain the mainstay of large thricobezoar removal 

Keywords: Bezoar; Trichotilomania; Tricotillofagia; Trichobezoar; Rapunzel Syndrome