Background: Rapunzel syndrome is an extremely rare 
intestinal condition in humans resulting from eating hair 
(trichophagia) . Rapunzel syndrome presents a rare type of 
trichobezoar with an extension of the hair into small bowel 
Case presentation: We present a three year old girl with 
Rapunzel syndrome, where the trichobezoar was not 
suspected at all. The history of disease was similiar with 
celiac disease even though serology was negative. 
Conclusion: In children with a long history of 
gastrointestinal symptoms,upper digestive endoscopy is a 
cornerstone of Rapunzel syndrome as a diagnostic tool (in 
our case for another objective).Open surgery remain the 
mainstay of large thricobezoar removal 
Keywords: Bezoar; Trichotilomania; Tricotillofagia; 
Trichobezoar; Rapunzel Syndrome